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Cochlear Implant Program

 [en español]

 

WHAT IS A COCHLEAR IMPLANT?

A hearing aid is a device that amplifies sound. The amplified sound then travels down the ear canal, past the ear drum and middle ear bones, to the cochlea. A cochlear implant is an artificial hearing device, which transmits sound directly to the auditory nerve through electrical stimulation of the cochlea, bypassing the ear canal, ear drum, and middle ear bones.

Neither hearing aids nor a cochlear implant can return a person with hearing loss to a state of normal hearing, but both provide children with better access to sound. For certain children with profound hearing loss, where benefit from hearing aids has been severely limited, a cochlear implant may provide vast improvement in the ability to listen and learn to communicate through spoken language.

HOW DOES NORMAL HEARING WORK?

The ear is divided in three parts: the outer, middle, and inner ear. The part of the ear we see and the ear canal make up the external ear. The middle ear includes the ear drum (tympanic membrane) and three tiny bones (malleus, incus and stapes). The inner ear consists of the cochlea and the vestibule.

When sound enters the ear canal, it vibrates the eardrum. This vibration then travels through the middle ear bones to the oval window, which is connected to the cochlea. The cochlea is a snail shaped tunnel filled with liquid and lined with “hair cells”. When the sound vibration hits the oval window, it vibrates the liquid inside the cochlea, which “stimulates” the hair cells. The hair cells then send an electrical signal to the auditory nerve which then carries the sound information to the brain.

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NORMAL HEARING

STIMULATION THROUGH A COCHLEAR IMPLANT

1. Sound travels through the air in waves.

2. Sound waves enter the ear through the opening in the outer ear. 2. Sound waves enter the microphone.
3. Sound waves travel down the ear canal. 3. The microphone changes the sound waves into an electrical signal.
4. Sound waves hit the eardrum and cause it to vibrate. 4. The electrical signal travels down a cable to the speech processor.
5. The vibration of the eardrum causes the three bones of the middle ear to vibrate. 5. The speech processor changes the electrical signal into a digital code.
6. The vibration of the three middle ear bones is transferred to the cochlear. 6. The digital code travels back up the same cable to the external transmitter coil.
7. This causes the fluid inside the cochlea to move with each wave of vibration. 7. The external transmitter coil produces a radio signal which travels through the skin.
8. The movement of the fluid inside the cochlea moves the “hair cells,” which are nerve endings suspended in the cochlea. 8. The internal receiver picks up the radio signal and converts it back into an electrical signal.
9. The movement of the “hair cells” sends an electrical signal to the auditory nerve. 9. The electrical signal travels down a wire to the electrodes inside the cochlea which directly stimulate the auditory nerve.

10. The auditory nerve sends the signal to the brain.

11. The brain interprets the signal.

HOW DOES THE IMPLANT WORK?

cochlear implant deviceThe cochlear implant consists of several parts:

  • Microphone: “collects” the sound
     
  • Sound processor: receives the sound and changes it into an electrical signal. The audiologist programs the device through a computer to provide the best possible sound to the child.
  • Transmitter coil: Sound is then sent through a cable to the transmitter coil and passes through the skin as an FM signal to an internal receiver/stimulator (the only part which is surgically implanted). The transmitter coil is held in place on the head with a magnet over the internal receiver/stimulator.
     
  • The internal receiver/stimulator takes the FM signal and translates it back into an electrical signal. This electrical signal is then sent down a wire which has been surgically placed inside the cochlea. Electrodes on that wire then stimulate the auditory nerve (hearing nerve), which sends the information to the brain.

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WHO IS A COCHLEAR IMPLANT CANDIDATE?

Generally speaking, anyone above 12 months of age, with severe-to-profound sensorineural hearing loss in both ears (70 decibels or greater), who have limited benefit from hearing aids is a candidate for a cochlear implant. Typically, a trial period with hearing aids of at least three-to-six months is necessary to determine if the patient has limited benefit.

WHAT NEEDS TO BE DONE TO ASSESS IF MY CHILD IS A CANDIDATE?
Attention: Hearing aids and earmolds in good working condition must be worn to all appointments.

ü Audiological evaluation

Please bring previous results to the clinic. Even if your child has had extensive testing elsewhere, Rady Children’s Cochlear Implant Audiologists need to assess your child so that we can get a feel for how easily your child can learn the techniques used in programming a cochlear implant.

  • Audiogram with and without hearing aids
  • Speech perception test will help determine hearing aid functional benefit
  • Tympanograms to determine if your child has or has a tendency to have middle ear fluid
  • BAER/OAE for objective information regarding inner ear and auditory nerve function

ü Medical evaluation

A thorough history is taken in order to evaluate the cause of the hearing loss and to see whether there are any medical problems that may have an impact on the cochlear implant surgery. A complete clinical ENT exam is performed focusing on the ears. Other exams such as blood tests or eye exams are ordered if necessary.

  • CT scan
    If you have any X-rays such as a CT scan or MRI of the ears or head, please bring them to your visit. Otherwise, a CT scan of the temporal bones will be ordered to see if the ear has a good anatomy for implantation.

ü Speech and language evaluation

The purpose of this evaluation is to determine pre-implant communicative ability and develop realistic post-implant goals. Even a child who has no verbal skills may be evaluated for pre-conversational skills such as turn taking, eye contact, joint visual regard of a desired object, and reaching and pointing to express interest.

ü Developmental and psychological evaluation

Both parents must attend this evaluation along with the child. Bring copies of the child’s most recent Individualized Family Service Plan (“IFSP,” for children from birth to age three) or Individualized Education Plan (“IEP,” for children age three and older), most recent evaluations for the child’s educational program, and any other developmental evaluations.

This evaluation will determine non-verbal cognitive ability and family structure and support needed for post-implant follow-up. Each parent’s expectations for the cochlear implant are reviewed.

ü Educational evaluation

Regular communication between the educational program and the Cochlear Implant Team is vital for post implant success. Prior to the implant, the Educational Liaison will  contact your child’s early intervention specialist or school therapists, teachers and educational audiologists to obtain information to help determine your child’s functional benefit from amplification.

The medical evaluation is done on Thursday mornings, at the Hearing Clinic of Rady Children's Otolaryngology Department. All the other appointments are held at Rady Children's Audiology/Hearing Department.

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WHAT TO EXPECT FROM THE COCHLEAR IMPLANT

The hearing potential from a cochlear implant depends on many factors, which are unique to the individual. Qualities that increase the likelihood of successful outcome include young age, short duration of deafness, good family support, intensive auditory habilitation and speech-language intervention, as well as normal cognitive development.

On average, an infant or toddler who is implanted has a very good chance of developing enough spoken language to be able to be in a mainstreamed educational placement by Kindergarten. This is only with intensive auditory habilitation, speech-language intervention, and carry-over of language learning activities into the daily routines of the home. Despite being able to attend a regular Kindergarten classroom, many children may still need some assistance to be successful in school, such as an FM system coupled to their implant, preferential seating in the classroom, and captioning or note taking services.

Children who are implanted over the age of four-to-five years face more challenges than younger children. To develop spoken language these children often need visual cues, such as speech reading or signed language, in addition to the auditory information the implant can provide. They may need a special classroom setting or additional supports at school for many years in order to be successful.

There are some children for whom the cochlear implant may not be appropriate, and it may interfere with the child's acquisition of signed language. These tend to be older children who have very limited spoken language and rely on signed language completely for communication.

Other developmental problems can make learning any language (spoken or signed) very difficult for a child. It is important to assess all aspects of the child’s development during the cochlear implant pre-evaluation process.

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HOW IS THE SURGERY DONE?

ü PRE-OP

The doctor will evaluate if there are any medical concerns. She will make sure your child has been vaccinated against HIB (Haemophilus influenzae) and Pneumococcus. This is mandatory, as these bacteria can cause meningitis (see complications). She will also check the CT scan to evaluate if there are any abnormalities in the ears, and choose the most appropriate side to be implanted.

ü SURGERY TECHNIQUE

If there are no major concerns, the cochlear implant is done as an outpatient procedure. The surgery is done under general anesthesia and takes about three hours. An incision is performed behind the ear to be implanted (see picture). The bone behind the ear canal (mastoid) is opened until we can see the middle ear. Another opening is done in the facial recess to visualize the round window, which is the opening to the cochlea. A small opening into the cochlea is made close to the round window and the implant electrode is placed inside the cochlea through this opening. The implant itself is held in place over the bone about one-to-two inches behind the ear. An X-ray is always obtained to assure that the electrode is in the right position. The surgical site is closed with absorbable sutures, and a dressing is applied that is removed the day after the surgery.

ü POST-OP

  • Most children experience only mild-to-moderate pain after the surgery
  • There may be some swelling behind the operated ear – this subsides in a few days. After the swelling subsides, in a few weeks-to-months, you will be able to feel a lump where the implanted device is located. This is normal.
  • Some children experience some imbalance after implant surgery. It is usually temporary.
  • A follow-up visit is scheduled 1 week after the surgery.

IMPORTANT:

  • ELECTROSURGICAL INSTRUMENTS (such as surgical cauteries) CANNOT BE USED IN THE HEAD AND NECK AREA AFTER IMPLANTATION.
  • IF AN MRI IS NEEDED AFTER IMPLANTATION, THE MAGNET INSIDE THE IMPLANT NEEDS TO BE REMOVED TEMPORARILY FOR THE EXAM (a small surgery is needed for that).

COMPLICATIONS

  • Anesthesia complications, same as for any other surgery
  • Facial nerve paralysis, temporary or permanent (rare)
  • Slight loss of taste sensation on the side of the surgery
  • Dizziness
  • Infection of the surgical site
  • Bleeding at the surgical site
  • Extrusion of the implant
  • Meningitis: a child who has a cochlear implant has a risk 30 times greater of developing meningitis than other children. This risk can be decreased by making sure the child has had all HIB (Haemophilus influenzae) and Pneumococcus vaccines prior to the surgery and by treating any ear infection aggressively after surgery.

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IS MY CHILD GOING TO HEAR RIGHT AFTER SURGERY? WHAT HAPPENS NEXT?

The implant is activated by the audiologist about one month after the surgery, when the surgical site has healed. After the first activation is when the real work starts. Here’s what needs to be done in order for your child to fully benefit from the cochlear implant:

ü Audiology

After the date of surgery is known, your child will be scheduled for “mapping” sessions of the external device (when the device is programmed using a computer). This typically consists of initial programming one month after surgery, with three-to-four more visits in the next month. After this period of initial programming, the child typically comes in twice every three months until one year after the implant surgery, and then every six months after that. These appointments are all necessary even if you think your child is doing well. “Mapping” appointments are quite long, two-hours or more for each session, because speech perception testing must be performed with the actual mapping being conducted afterward to incorporate any information obtained during the speech perception testing. Parents should ensure that their child has had adequate rest and nutrition prior to these appointments.

ü Speech and Language

Typically it is recommended after implant surgery that a child receive auditory habilitation and speech-language intervention at the hospital, in addition to what is provided in the educational program, for a minimum of one year. This treatment usually consists of two sessions per week. The speech-language pathologist will re-evaluate the need for continued therapy at regular intervals.  Some kids continue throughout their education.

ü Education

An educational program which emphasizes learning spoken language through listening is strongly recommended. If the child has used signed language in the past, a transitional period may be necessary in which both signed and spoken language are used in the educational program, but plans should be made to increase the emphasis on listening throughout the child’s daily routines at home and/or throughout the school day. 

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RADY CHILDREN’S HOSPITAL OF SAN DIEGO COCHLEAR IMPLANT TEAM


Back (left to right): Brooke Stulz, Ellie Kalter, Catherine Dabasinskas, Jackie Rand, Alyson Mellish, Shani Goldgrub and James "Kim" Wilkes
Front (left to right): Melanie Coll, Daniela Carvalho, Alyssa Needleman, Rada West, Valerie Dorfman, Ayala Ben-Tall, and Jennifer Foss.

Ayala Ben-Tall, Ph.D., is a psychologist who received her Ph.D. from the University of California, Santa Barbara in 1998. She has worked at the Rady Children’s Hospital Developmental Evaluation Clinic and has been on the Cochlear Implant Team since 2000.

Daniela Carvalho, M.D. is our ENT surgeon. She did her ENT-Head and Neck surgery residency in Brazil and completed a pediatric otolaryngology fellowship at Rady Children’s Hospital-San Diego from 1999 to 2001. She was invited to join the pediatric ENT practice at Rady Children’s Hospital as the ear specialist. She is the director of the Hearing Program at Rady Children’s Hospital. She has published extensively in pediatric otolaryngology and has been invited to speak at meetings in the USA and other countries. Dr. Carvalho speaks five languages, including English, Spanish, Portuguese, French and German.

Melanie Coll has worked as an audiologist since August 2005, when she joined Rady Children's Audiology team. Melanie has special skills in pediatric testing and hearing aid fitting. She has experience using American Sign Language and working with the culturally Deaf population. Her clinical fellowship year was spent at the Children's National Medical Center in Washington, DC. Other areas of interest are Cochlear Implants.

Catherine Dabasinskas has worked at Rady Children's since 2001. She specializes in working with children with hearing loss, cochlear implants, multiple disabilities, autism and dyspraxia.

Valerie Dorfman joined Rady Children's Hospital in March 2008. Prior to working in the hospital's outpatient setting, she worked in several public schools and outpatient hospital settings in Massachusetts. Valerie received her Master of Science in Speech Language Pathology at Boston University. She is a native Spanish speaker and specializes in providing therapy in Spanish. Her interests include working with children with hearing loss, cochlear implants, cleft lip and palate, speech and language impairments, apraxia of speech, and Autism Spectrum Disorders.

Jennifer Foss has worked at Rady Children's Hospital since June 2006. Jennifer has experience working with a variety of children and adults with communication disorders, including those with speech and language delays, apraxia of speech, autism spectrum disorders, cleft palate, cochlear implants, acquired traumatic brain injuries, voice, and stuttering.

Shani Goldgrub joined the Audiology team at Rady Children's in 2007, when she completed her clinical doctorate degree in Audiology. Shani completed her clinical externship at Providence Speech and Hearing Center in Orange, California, where she gained experience in pediatric Audiology, hearing aids and auditory evoked potentials. Additionally, she has special interest in cochlear implants. Having been raised in Mexico, Shani is fluent in Spanish.

Eleanor Kalter became a speech-language pathologist in 1984 and joined Rady Children's in 1989. Eleanor has special talents in bilingual/bicultural therapy and consultation on related issues.  Her extensive background includes working in Spanish and French as well as with other multicultural populations. Eleanor also has expertise in treating children with cleft palate and craniofacial anomalies, having served as speech pathologist on the Rady Children's Craniofacial team for over 10 years.

Alyson Mellish, Au.D. has been an audiologist since 2002 and has worked at Rady Children's since July 2004. She specializes in the areas of pediatric diagnostic Audiology, hearing aid dispensing, and cochlear implant evaluations and rehabilitation.  Dr. Mellish also serves as the Cochlear Implant Team Educational Liaison, collaborating between the clinic and the classroom.

Alyssa Needleman, Ph.D., leads the Audiology Department at Rady Children's Hospital San Diego, providing day to day leadership to the department and developing systems that ensure quality patient care outcomes and fiscal management. She earned her doctorate at the University of Texas at Dallas, with her area of expertise in speech perception in individuals with hearing loss. She is certified as an audiologist with the American Speech-Language-Hearing Association, is a Fellow of the American Academy of Audiology, and has worked in all aspects of the audiological community since 1991, including hospital, corporate and university settings, as well as running her own private practice.

Jackie Rand, Hearing Aid Program Coordinator, has worked in the health care field for 30 years in a variety of different areas, including Health Education in the private sector as Program Coordinator of a Health Prevention program for employees.  She also worked for Sharp Healthcare for 19 of those 30 years in Physical Rehabilitation, Marketing and Volunteer Services. Jackie came to Rady Children’s hospital in March of 2005 as Hearing Aid Program Coordinator and since that time has done a wonderful job working with the Cochlear Implant team. Her goal is to provide the best possible service for our patients and families and to ensure that any equipment necessary is made available to them.

Brooke Stulz joined Rady Children's Hospital in September 2005. Prior to working in the hospital's outpatient/inpatient setting, she was a school speech therapist in the U.S. Virgin Islands School District. Brooke specializes in early intervention, early childhood language, apraxia, articulation, and Autism Spectrum Disorders.

Rada West, Ph.D. has been a licensed clinical psychologist since 2006 and has worked at Rady Children's Hospital Developmental Evaluation Clinic since 2005, specializing in neuropsychological and developmental evaluations of young children with developmental disabilities, Autism, learning disabilities and children who are preparing to receive a cochlear implant. She has been a part of the Cochlear Implant Team since 2007. She is bilingual in English and Russian.

James Kim Wilkes, Ph.D. has been a psychologist since 1990. He has worked at Rady Children's since 1988 and specializes in the areas of developmental assessments of infants, preschoolers, children in foster care, and children preparing to receive cochlear implants. He received his doctorate in psychology at the California School of Professional Psychology, San Diego in 1987.

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LINKS

Cochlear Implant association, Inc. is a is a non-profit organization for cochlear implant recipients, their families, professionals, and other individuals interested in cochlear implants.
http://www.cici.org/

British Cochlear implant group
http://www.bcig.org/

NIDCD: National Institute on Deafness and Other Communication Disorders
http://www.nidcd.nih.gov/health/hearing/coch.asp

CONTACT US

If you have any questions or would like to make an appointment, please call 858-966-5838 or 858-495-7767 (TTY).


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